Melanotic neuroectodermal tumor of infancy: a rare presentation of an extremely rare neoplasm and diagnostic implications in Gombe, Nigeria
نویسندگان
چکیده
Melanotic neuro-ectodermal tumor of infancy is very rare. A unique neoplasm of the formative years, it typically involves the face or cranium; possesses rapid, expansile growth; presents as a firm swelling and displays a high rate of recurrence. Its rarity and unique features make diagnosis and management quite challenging. This challenge is increased in resource-limited settings like ours and with atypical presentation, such as was seen at our center, where patient presented with a bony hard swelling.
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تومور ملانوتیک نورواکتودرمال در فک بالای شیرخوار هفت ماهه: یک گزارش مورد
Background and Objectives: Melanotic neuroectodermal tumor of infancy (MNTI) is a rare, usually benign neoplasm of neural crest origin. MNTI usually arises in infants within the first year of life. The tumor is usually observed in head and neck areas especially in maxilla; however it has been reported in other areas such as hip, bone marrow, and ovary as well. It usually appears as a ...
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متن کاملMelanotic neuroectodermal tumour of infancy.
Melanotic neuroectodermal tumour of infancy is an extremely rare neoplasm arising in newborns and young children, typically involving the face or cranium. A case arising from the maxilla, requiring extensive resection with a near-total maxillectomy, is presented. A thorough review of the literature on this unusual tumour is provided, with emphasis on prognostic factors and appropriate treatment.
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عنوان ژورنال:
دوره 28 شماره
صفحات -
تاریخ انتشار 2017